Boli cardiovasculare genetice

Curs Boli Cardiovasculare Genetice – 4 aprilie 2019

Directori de curs:

Ruxandra Jurcuţ, Carmen Ginghină

 

9.00 – 10.30 – Cardiomiopatii genetice (Genetic cardiomyopathies)

Moderatori: Carmen Ginghină, Juan Ramon Gimeno

  • Genetica ȋn ghidarea terapiei ȋn cardiomiopatii (Genetics for therapeutic guidance) – Ruxandra Jurcuţ
  • Biomarkeri in cardiomiopatii genetice (Biomarkers in genetic cardiomyopathies) – Carmen Ginghină
  • Fibrilatia atriala in cardiomiopatii – de la risc tromboembolic la terapie (Atrial fibrillation in cardiomyopathies – from thromboembolic risk to therapy) – Ioan Mircea Coman
  • Terapia aritmii ventriculare in cardiomiopatii (Ventricular arrhythmias management in cardiomyopathies) – Radu Vătăşescu

 

11.00 – 12.30 – Ce este nou in cardiomiopatii genetice (What is new in genetic cardiomyopathies)

Moderatori: Ruxandra Jurcut, Thibaud Damy

  • Cardiomiopatia hipertrofică (Hypertrophic cardiomyopathy) – Juan Ramon Gimeno (Spania)
  • Amiloidoza (Amyloidosis) – Thibaud Damy (Franta)
  • Boala Fabry (Fabry disease) – Ales Linhart (Cehia)
  • Cardiomiopatia dilatativă familială (Familial dilated cardiomyopathy) – Silvia Oghina (Franta)

 

13.30 – 15.00 – Boala Marfan (Marfan syndrome)

Moderatori: Guillaume Jondeau, Zoltan Szabolcs

  • Aspecte clinice ȋn sindromul Marfan (Clinical aspects of Marfan syndrome) Laurence Campens (Belgia)
  • Anevrismul de aorta toracică: de la stratificarea riscului la terapie (Thoracic ascending aortic aneurysms: How to tailor the indications to patient risk; medical therapy) Guillaume Jondeau (Franta)
  • Tratament chirurgical in boala Marfan (Root sparing cardiovascular surgery in Marfan disease) – Vlad Iliescu
  • SItuaţii chirurgicale speciale datorate anomaliilor toracice severe (Surgical considerations during aortic root surgey  in case of coexistent severe chest abnormalities in Marfan patients) Zoltan Szabolcs (Ungaria)

 

15.30-17.00 – Sesiune de cazuri clinice (Clinical case session)

Moderatori: Ruxandra Jurcut, Ioan Mircea Coman

  • Boala Marfan in sarcina – Laurence Campens, Belgia
  • Cardiomiopatie hipertrofică – Monica Roşca, Bucureşti
  • Cardiomiopatie hipertrofică – nu sunt două la fel! – Attila Frigy, Tg Mureş
  • Amiloidoză TTR – Robert Adam, Bucureşti
  • Cardiomiopatie aritmogenă de ventricul drept – Radu Sascău, Iaşi